Question

how do you think sex is determined in a person with chromosomal disorder involving the sex chromosomes

Answer 1

 It's pretty much that if you have a Y chromosome, you are male. 

X, XX, XXX, XXXX, XXXXX, etc female 
Y - incompatible with life 
XY, XXY, XXXY, XXXXY, etc - male. 
XXYY - male